Physical Medicine Interventions for Duchenne Muscular Dystrophy, the Including Avoiding Invasive Airway Tubes

Introduction 7
Stage 1: Ambulatory 9
Interventions to Optimize Habilitation 9
Stage 2: Wheelchair use 13
Prevention of Spinal Deformity and Preparation of Surgery 13
Patients are Evaluated for use of Physical Medicine Respiratory Muscle Aids 14
Evaluation 14
Interventions in Stage 2 15
Stage 3: Prolongation of life with quality and without airway tubes 18
Continuously Maintain Normal Pulmonary Ventilation 18
Inspiratory Muscle Aids 19
Extubation and Decannulation to Definitively Avoid Tracheostomies 22
Quality of Life 22
Key points 24
References 25

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